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KMID : 0882420060700050564
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Korean Journal of Medicine
2006 Volume.70 No. 5 p.564 ~ p.568
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A case of KearnsSayre syndrome complicated with complete AV block
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박인혜/Park IH
임종근/문정근/정보영/이문형/김성순/Lim JK/Moon JG/Joung BY/Lee MH/Kim SS
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Abstract
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KearnsSayre syndrome (KSS) is a mitochondrial DNA disorder characterized by the onset before age 20 years, progressive external opthalomoplegia, atypical retinal pigmentation and cardiac conduction disturbance. This report describes a 24-year-old woman who experienced syncope due to complete atrioventricular block complicated by KSS. At 12 years old, she was diagnosed KSS. The consecutive change of EKG shows typical progression of cardiac conduction disturbance of KSS. She was successfully treated with implantation of a pacemaker.
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KEYWORD
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